Cystic Fibrosis

Displaying 1 - 39 of 39CSV
Jorth, P., Manuel, C., McLemore, T., Humphries, R. M., Cole, N. C., Schuetz, A. N., Garica, D., Maldonado, M., Rivero, N., Milesi Galdino, A. C., Celedonio, D., LiPuma, J. J., Green, D. A., Zlosnik, J. E. A., Traczewski, M., & Huse, H. K. (2025). Evaluation of antimicrobial susceptibility testing methods for Burkholderia cepacia complex isolates from people with and without cystic fibrosis. Journal of Clinical Microbiology. https://doi.org/10.1128/jcm.01480-24
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Zuckerman, J. B., Hinton, A. C., Lahiri, T., Teneback, C. C., Jia, S., Mermis, J., Polineni, D., Dasenbrook, E., Sadeghi, H., DiMango, E., Dezube, R., West, N. E., Zemanick, E. T., Samya, Z. N., & Gifford, A. H. (2025). C‐Reactive Protein Changes in Adult and Pediatric People With Cystic Fibrosis During Treatment of Pulmonary Exacerbations. Pediatric Pulmonology, 60(1). Portico. https://doi.org/10.1002/ppul.27487
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Keating, C., Yonker, L. M., Vermeulen, F., Prais, D., Linnemann, R. W., Trimble, A., Kotsimbos, T., Mermis, J., Braun, A. T., O’Carroll, M., Sutharsan, S., Ramsey, B., Mall, M. A., Taylor-Cousar, J. L., McKone, E. F., Tullis, E., Floreth, T., Michelson, P., Sosnay, P. R., … Horsley, A. (2025). Vanzacaftor–tezacaftor–deutivacaftor versus elexacaftor–tezacaftor–ivacaftor in individuals with cystic fibrosis aged 12 years and older (SKYLINE Trials VX20-121-102 and VX20-121-103): results from two randomised, active-controlled, phase 3 trials. The Lancet Respiratory Medicine. https://doi.org/10.1016/s2213-2600(24)00411-9
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Burdis, N., Milinic, T., Bartlett, L. E., Goss, L., Tallarico, E., Boyle, A., Thaxton, A., Turner, G. A., Benvenuto, L. J., Faro, A., Goss, C. H., Kapnadak, S. G., & Ramos, K. J. (2024). A survey of cystic fibrosis physicians’ views on lung transplant referral in the era of elexacaftor/tezacaftor/ivacaftor. Pediatric Pulmonology, 59(12), 3641–3649. Portico. https://doi.org/10.1002/ppul.27273
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Saiman, L., Waters, V., LiPuma, J. J., Hoffman, L. R., Alby, K., Zhang, S. X., Yau, Y. C., Downey, D. G., Sermet-Gaudelus, I., Bouchara, J.-P., Kidd, T. J., Bell, S. C., & Brown, A. W. (2024). Practical Guidance for Clinical Microbiology Laboratories: Updated guidance for processing respiratory tract samples from people with cystic fibrosis. Clinical Microbiology Reviews, 37(3). https://doi.org/10.1128/cmr.00215-21
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Kay, D. M., Sadeghi, H., Kier, C., Berdella, M., DeCelie‐Germana, J. K., Soultan, Z. N., Goetz, D. M., Caggana, M., Fortner, C. N., Giusti, R., Kaslovsky, R., Stevens, C., Voter, K., Welter, J. J., & Langfelder‐Schwind, E. (2024). Genetic counseling access and service delivery in New York State is variable for parents of infants with complex CFTR genotypes conferring uncertain phenotypes. Pediatric Pulmonology, 59(7), 1952–1961. Portico. https://doi.org/10.1002/ppul.27023
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Rose, N. R., Chalamalla, A. R., Garcia, B. A., Krick, S., Bergeron, J., Sadeghi, H., Schellhase, D. E., Ryan, K. J., Dowell, A. E., Acosta, E. P., & Guimbellot, J. S. (2024). Pharmacokinetic variability of CFTR modulators from standard and alternative regimens. Pulmonary Pharmacology & Therapeutics, 86, 102301. https://doi.org/10.1016/j.pupt.2024.102301
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McDonald, C. M., Reid, E. K., Pohl, J. F., Yuzyuk, T. K., Padula, L. M., Vavrina, K., & Altman, K. (2024). Cystic fibrosis and fat malabsorption: Pathophysiology of the cystic fibrosis gastrointestinal tract and the impact of highly effective CFTR modulator therapy. Nutrition in Clinical Practice, 39(S1). Portico. https://doi.org/10.1002/ncp.11122
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Miller, J. E., Taylor‐Cousar, J. L., Overdevest, J. B., Khatiwada, A., Mace, J. C., Alt, J. A., Bodner, T. E., Chowdhury, N. I., DiMango, E. A., Eshaghian, P. H., Getz, A. E., Gudis, D. A., Han, E. J., Hwang, P. H., Keating, C. L., Khanwalkar, A., Kimple, A. J., Lee, J. T., Li, D., … Beswick, D. M. (2023). Determining the minimal clinically important difference for the questionnaire of olfactory disorders in people with cystic fibrosis and factors associated with improvement after highly effective modulator therapy. International Forum of Allergy & Rhinology, 14(6), 1079–1087. Portico. https://doi.org/10.1002/alr.23312
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Tervo, J. P., DiMango, E., Gudis, D. A., Keating, C., Zhang, Y., Leu, C., Altman, K., Vilarello, B., Jacobson, P., & Overdevest, J. B. (2023). Olfaction, body mass index, and quality of life with cystic fibrosis combination therapy. International Forum of Allergy & Rhinology, 13(12), 2165–2171. Portico. https://doi.org/10.1002/alr.23209
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List, R., Solomon, G., Bichl, S., Horton, B. J., Shen, S., Corcoran, B., Sadeghi, H., Britto, M. T., Ren, C., & Albon, D. (2023). Improved recognition of lung function decline as signal of cystic fibrosis pulmonary exacerbation: a Cystic Fibrosis Learning Network Innovation Laboratory quality improvement initiative. BMJ Open Quality, 12(4), e002466. https://doi.org/10.1136/bmjoq-2023-002466
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Shah, K. S., Saiman, L., LiPuma, J. J., Kosorok, M. R., & Muhlebach, M. S. (2024). Association of Pseudomonas aeruginosa incident infections with adherence to cystic fibrosis foundation care guidelines. Journal of Cystic Fibrosis, 23(2), 300–305. https://doi.org/10.1016/j.jcf.2023.10.015
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Melton, K., Liu, J., Sadeghi, H., George, M., & Smaldone, A. (2024). Predictors of Transition Outcomes in Cystic Fibrosis: Analysis of National Patient Registry and CF RISE (Responsibility. Independence. Self-care. Education) Data. The Journal of Pediatrics, 265, 113812. https://doi.org/10.1016/j.jpeds.2023.113812
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Mayer-Hamblett, N., Clancy, J. P., Jain, R., Donaldson, S. H., Fajac, I., Goss, C. H., Polineni, D., Ratjen, F., Quon, B. S., Zemanick, E. T., Bell, S. C., Davies, J. C., Jain, M., Konstan, M. W., Kerper, N. R., LaRosa, T., Mall, M. A., McKone, E., Pearson, K., … Downey, D. G. (2023). Advancing the pipeline of cystic fibrosis clinical trials: a new roadmap with a global trial network perspective. The Lancet Respiratory Medicine, 11(10), 932–944. https://doi.org/10.1016/s2213-2600(23)00297-7
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Leonard, A., Bailey, J., Bruce, A., Jia, S., Stein, A., Fulton, J., Helmick, M., Litvin, M., Patel, A., Powers, K. E., Reid, E., Sankararaman, S., Clemm, C., Reno, K., Hempstead, S. E., & DiMango, E. (2023). Nutritional considerations for a new era: A CF foundation position paper. Journal of Cystic Fibrosis, 22(5), 788–795. https://doi.org/10.1016/j.jcf.2023.05.010
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Gifford, A. H., Hinton, A. C., Jia, S., Nasr, S. Z., Mermis, J. D., Lahiri, T., Zemanick, E. T., Teneback, C. C., Flume, P. A., DiMango, E. A., Sadeghi, H., Polineni, D., Dezube, R. H., West, N. E., Dasenbrook, E. C., Lucas, F. L., & Zuckerman, J. B. (2023). Complications and Practice Variation in the Use of Peripherally Inserted Central Venous Catheters in People With Cystic Fibrosis. CHEST, 164(3), 614–624. https://doi.org/10.1016/j.chest.2023.03.043
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South, K., Smaldone, A., Sadeghi, H., Piane, V., Kowal, R., Wei, L., & George, M. (2023). Parent and adolescent perceptions of cystic fibrosis management responsibility: A mixed‐methods study. Pediatric Pulmonology, 58(8), 2340–2351. Portico. https://doi.org/10.1002/ppul.26494
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Baldwin-Hunter, B. L., Rozenberg, F. D., Annavajhala, M. K., Park, H., DiMango, E. A., Keating, C. L., Uhlemann, A.-C., & Abrams, J. A. (2023). The gut microbiome, short chain fatty acids, and related metabolites in cystic fibrosis patients with and without colonic adenomas. Journal of Cystic Fibrosis, 22(4), 738–744. https://doi.org/10.1016/j.jcf.2023.01.013
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Uluer, A. Z., MacGregor, G., Azevedo, P., Indihar, V., Keating, C., Mall, M. A., McKone, E. F., Ramsey, B. W., Rowe, S. M., Rubenstein, R. C., Taylor-Cousar, J. L., Tullis, E., Yonker, L. M., Chu, C., Lam, A. P., Nair, N., Sosnay, P. R., Tian, S., Van Goor, F., … Wilson, J. (2023). Safety and efficacy of vanzacaftor–tezacaftor–deutivacaftor in adults with cystic fibrosis: randomised, double-blind, controlled, phase 2 trials. The Lancet Respiratory Medicine, 11(6), 550–562. https://doi.org/10.1016/s2213-2600(22)00504-5
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Kass, A. P., Kazmerski, T. M., Bern, E., Sabharwal, S., Leonard, J., Harrison, M., Barnico, K., Richmond, T., & Sawicki, G. S. (2023). Clinician perspectives on assessing for disordered eating and body image disturbance in adolescents and young adults with cystic fibrosis. Journal of Cystic Fibrosis, 22(3), 431–435. https://doi.org/10.1016/j.jcf.2022.11.006
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Altamimi, E., Rabab’h, O., Aburizeg, D., Akasheh, L., Dardas, Z., Srour, L., Awad, H., & Azab, B. (2022). Investigating the genetic profile of familial atypical cystic fibrosis patients (DeltaF508-CFTR) with neonatal biliary atresia. Journal of Applied Genetics, 64(1), 71–80. https://doi.org/10.1007/s13353-022-00729-5
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Knotts, R. M., Jin, Z., Doyle, J. B., Keating, C., DiMango, E., & Abrams, J. A. (2022). Body mass index and additional risk factors for cancer in adults with cystic fibrosis. Cancer Causes & Control, 33(12), 1445–1451. https://doi.org/10.1007/s10552-022-01635-1
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Caverly, L. J., Riquelme, S. A., & Hisert, K. B. (2022). The Impact of Highly Effective Modulator Therapy on Cystic Fibrosis Microbiology and Inflammation. Clinics in Chest Medicine, 43(4), 647–665. https://doi.org/10.1016/j.ccm.2022.06.007
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Kass, A. P., Berbert, L., Dahlberg, S., Bern, E., Sabharwal, S., Leonard, J., Richmond, T., & Sawicki, G. S. (2022). Eating disorders in adolescents and young adults with cystic fibrosis. Pediatric Pulmonology, 57(11), 2791–2797. Portico. https://doi.org/10.1002/ppul.26102
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Schmidt, C. N., Friedman, A. M., DiMango, E. A., Linder, A. H., Sobhani, N. C., D’Alton, M. E., & Wen, T. (2022). Trends in and Outcomes of Deliveries Complicated by Cystic Fibrosis. Obstetrics & Gynecology, 140(5), 861–868. https://doi.org/10.1097/aog.0000000000004959
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Pinezich, M. R., Tamargo, M. A., Fleischer, S., Reimer, J. A., Hudock, M. R., Hozain, A. E., Kaslow, S. R., Tipograf, Y., Soni, R. K., Gavaudan, O. P., Guenthart, B. A., Marboe, C. C., Bacchetta, M., O’Neill, J. D., Dorrello, N. V., & Vunjak-Novakovic, G. (2022). Pathological remodeling of distal lung matrix in end-stage cystic fibrosis patients. Journal of Cystic Fibrosis, 21(6), 1027–1035. https://doi.org/10.1016/j.jcf.2022.04.016
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Stoudemire, W., Jiang, X., Zhou, J. J., Kosorok, M. R., Saiman, L., & Muhlebach, M. S. (2022). Predicting risk-adjusted incidence rates of methicillin-resistant Staphylococcus Aureus and Pseudomonas Aeruginosa in cystic fibrosis programs in the United States. Journal of Cystic Fibrosis, 21(6), 1013–1019. https://doi.org/10.1016/j.jcf.2022.08.002
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Lloyd, E. C., Cogen, J. D., Maples, H., Bell, S. C., & Saiman, L. (2022). Antimicrobial Stewardship in Cystic Fibrosis. Journal of the Pediatric Infectious Diseases Society, 11(Supplement_2), S53–S61. https://doi.org/10.1093/jpids/piac071
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Spielman, D. B., Beswick, D. M., Kimple, A. J., Senior, B. A., Aanaes, K., Woodworth, B. A., Schlosser, R. J., Lee, S., Cho, D., Adappa, N. D., DiMango, E., & Gudis, D. A. (2022). The management of cystic fibrosis chronic rhinosinusitis: An evidenced‐based review with recommendations. International Forum of Allergy & Rhinology, 12(9), 1148–1183. Portico. https://doi.org/10.1002/alr.22953
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Kimple, A. J., Senior, B. A., Naureckas, E. T., Gudis, D. A., Meyer, T., Hempstead, S. E., Resnick, H. E., Albon, D., Barfield, W., Benoit, M. M., Beswick, D. M., Callard, E., Cofer, S., Downer, V., Elson, E. C., Garinis, A., Halderman, A., Hamburger, L., Helmick, M., … Lee, S. E. (2022). Cystic Fibrosis Foundation otolaryngology care multidisciplinary consensus recommendations. International Forum of Allergy & Rhinology, 12(9), 1089–1103. Portico. https://doi.org/10.1002/alr.22974
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Stick, S. M., Foti, A., Ware, R. S., Tiddens, H. A. W. M., Clements, B. S., Armstrong, D. S., Selvadurai, H., Tai, A., Cooper, P. J., Byrnes, C. A., Belessis, Y., Wainwright, C., Jaffe, A., Robinson, P., Saiman, L., & Sly, P. D. (2022). The effect of azithromycin on structural lung disease in infants with cystic fibrosis (COMBAT CF): a phase 3, randomised, double-blind, placebo-controlled clinical trial. The Lancet Respiratory Medicine, 10(8), 776–784. https://doi.org/10.1016/s2213-2600(22)00165-5
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Murray, L., & Saiman, L. (2022). Potential opportunities and challenges for infection prevention and control for cystic fibrosis in the modern era. Current Opinion in Infectious Diseases, 35(4), 346–352. https://doi.org/10.1097/qco.0000000000000847
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South, K., George, M., Sadeghi, H., Piane, V., & Smaldone, A. (2022). Moving up: Healthcare transition experiences of adolescents and young adults with cystic fibrosis. Journal of Pediatric Nursing, 65, 116–123. https://doi.org/10.1016/j.pedn.2022.03.007
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Simonson, J. L., Esposito, C., Frantzen, T., Henthorne, K., Espinal, A., Romano, S., Ramdeo, R., Trentacoste, J., Tsang, D., LaVecchia, G., Abdullah, R., Berdella, M., Bonitz, L., Condos, R., Constantinescu, A., DeCelie-Germana, J. K., DiMango, E., Draine, M., Gimeli, T., … Wang, J. (2022). The clinical impact of the Covid-19 pandemic first wave on patients with cystic fibrosis in New York. Journal of Cystic Fibrosis, 21(3), e176–e183. https://doi.org/10.1016/j.jcf.2022.02.012
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Gross, J. E., Caceres, S., Poch, K., Hasan, N. A., Davidson, R. M., Epperson, L. E., Lipner, E., Vang, C., Honda, J. R., Strand, M., Strong, M., Saiman, L., Prevots, D. R., Olivier, K. N., & Nick, J. A. (2021). Healthcare-associated links in transmission of nontuberculous mycobacteria among people with cystic fibrosis (HALT NTM) study: Rationale and study design. PLOS ONE, 16(12), e0261628. https://doi.org/10.1371/journal.pone.0261628
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