Z-α 1 -antitrypsin polymers impose molecular filtration in the endoplasmic reticulum after undergoing phase transition to a solid state

Chambers, J. E., Zubkov, N., Kubánková, M., Nixon-Abell, J., Mela, I., Abreu, S., Schwiening, M., Lavarda, G., López-Duarte, I., Dickens, J. A., Torres, T., Kaminski, C. F., Holt, L. J., Avezov, E., Huntington, J. A., George-Hyslop, P. S., Kuimova, M. K., & Marciniak, S. J. (2022). Z-α1-antitrypsin polymers impose molecular filtration in the endoplasmic reticulum after undergoing phase transition to a solid state. Science Advances, 8(14). https://doi.org/10.1126/sciadv.abm2094
Authors:
Joseph E. Chambers
Nikita Zubkov
Markéta Kubánková
Jonathon Nixon‐Abell
Ioanna Mela
Susana Abreu
Max Schwiening
Giulia Lavarda
Ismael López‐Duarte
Jennifer A. Dickens
Tomás Torres⊗
Clemens F. Kaminski
Liam J. Holt
Edward Avezov
James A. Huntington
Peter St George‐Hyslop
Marina K. Kuimova
Stefan J. Marciniak
Affiliated Authors:
Peter St George‐Hyslop
Publication Type:
Article
Unique ID:
10.1126/sciadv.abm2094
PMID:
Journal:
Publication Date:
Data Source:
OpenAlex

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