Pathological remodeling of distal lung matrix in end-stage cystic fibrosis patients

Pinezich, M. R., Tamargo, M. A., Fleischer, S., Reimer, J. A., Hudock, M. R., Hozain, A. E., Kaslow, S. R., Tipograf, Y., Soni, R. K., Gavaudan, O. P., Guenthart, B. A., Marboe, C. C., Bacchetta, M., O’Neill, J. D., Dorrello, N. V., & Vunjak-Novakovic, G. (2022). Pathological remodeling of distal lung matrix in end-stage cystic fibrosis patients. Journal of Cystic Fibrosis, 21(6), 1027–1035. https://doi.org/10.1016/j.jcf.2022.04.016
Authors:
Meghan R Pinezich
Manuel A Tamargo
Sharon Fleischer
Jonathan A Reimer
Maria R Hudock
Ahmed E Hozain
Sarah R Kaslow
Yuliya Tipograf
Rajesh Kumar Soni
Olimpia P Gavaudan
Brandon A Guenthart
Charles C Marboe
Matthew Bacchetta
John D O'Neill
N Valerio Dorrello
Gordana Vunjak-Novakovic
Affiliated Authors:
Meghan R Pinezich
Manuel A Tamargo
Sharon Fleischer
Jonathan A Reimer
Maria R Hudock
Ahmed E Hozain
Sarah R Kaslow
Rajesh Kumar Soni
Olimpia P Gavaudan
Charles C Marboe
N Valerio Dorrello
Gordana Vunjak-Novakovic
Subjects:
Author Keywords:
cystic fibrosis
extracellular matrix
lung proteases
basement membrane
biomarkers
Publication Type:
Article
Unique ID:
10.1016/j.jcf.2022.04.016
PMID:
Publication Date:
Data Source:
PubMed

Record Created: